Overview
Definition
Multi-system vasculitis.
Epidemiology
Varies globally depending on genetics, environment, or exposure.
Etiology & Risk Factors
- Autoimmune, strongly associated with HLA-B51.
Clinical Symptoms
- Recurrent painful oral ulcers
- genital ulcers
- uveitis.
Clinical Approach
Diagnosis
- Clinical diagnosis
- Pathergy test.
Management
- Colchicine
- Corticosteroids
- Biologics.
Complications
- Blindness
- neurologic involvement.