Dermatitis Herpetiformis

Dermatology

Overview

Definition

Intensely pruritic vesicular rash associated with Celiac disease.

Epidemiology

Varies globally depending on genetics, environment, or exposure.

Etiology & Risk Factors

  • IgA deposition in the dermal papillae.

Clinical Symptoms

  • Grouped
  • intensely itchy vesicles on elbows
  • knees
  • and buttocks.

Clinical Approach

Diagnosis

  • Skin biopsy with direct immunofluorescence.

Management

  • Strict Gluten-Free Diet
  • Dapsone (for rapid relief).

Complications

  • GI lymphoma (if Celiac disease untreated).