Overview
Definition
Inflammatory myopathy with skin manifestations.
Epidemiology
Varies globally depending on genetics, environment, or exposure.
Etiology & Risk Factors
- Autoimmune.
Clinical Symptoms
- Proximal muscle weakness
- Heliotrope rash (eyelids)
- Gottron papules (knuckles).
Clinical Approach
Diagnosis
- High CK/Aldolase
- Anti-Jo-1
- Muscle biopsy.
Management
- Systemic corticosteroids
- Immunosuppressants.
Complications
- Strong association with underlying malignancy.