Overview
Definition
Vasculitis affecting small/medium vessels, associated with asthma.
Epidemiology
Varies globally depending on genetics, environment, or exposure.
Etiology & Risk Factors
- Autoimmune (p-ANCA/MPO-ANCA positive in ~40%).
Clinical Symptoms
- Adult-onset asthma
- allergic rhinitis
- peripheral neuropathy (mononeuritis multiplex).
Clinical Approach
Diagnosis
- Tissue biopsy (eosinophilic granulomas).
Management
- High-dose corticosteroids.
Complications
- Nerve damage
- cardiac involvement.