Glioblastoma Multiforme

Oncology

Overview

Definition

Most aggressive and common primary malignant brain tumor.

Epidemiology

Highest incidence in adults > 50 years. Very poor prognosis.

Etiology & Risk Factors

  • Mostly de novo
  • Prior radiation
  • Genetic syndromes (Li-Fraumeni)

Clinical Symptoms

  • Headache (worse in morning)
  • Seizures
  • Focal neurologic deficits
  • Personality changes

Clinical Approach

Diagnosis

  • MRI Brain with contrast (ring-enhancing lesion with central necrosis crossing corpus callosum - butterfly glioma)

Management

  • Maximal safe surgical resection
  • Radiation therapy
  • Temozolomide chemotherapy

Complications

  • Cerebral edema
  • Herniation
  • Death (median survival 15 months)