Overview
Definition
Glucagon-secreting tumor of the pancreas.
Epidemiology
Varies globally depending on genetics, environment, or exposure.
Etiology & Risk Factors
- Malignant neuroendocrine tumor.
Clinical Symptoms
- Mild diabetes
- Necrolytic migratory erythema (red blistering rash)
- weight loss
- DVT.
Clinical Approach
Diagnosis
- Markedly elevated fasting glucagon.
Management
- Octreotide
- Surgical resection.
Complications
- Metastasis (usually to liver).