Overview
Definition
Autoimmune disease affecting lungs and kidneys.
Epidemiology
Varies globally depending on genetics, environment, or exposure.
Etiology & Risk Factors
- Anti-GBM antibodies (Type II hypersensitivity).
Clinical Symptoms
- Hemoptysis
- dyspnea
- hematuria.
Clinical Approach
Diagnosis
- Renal biopsy (linear IgG deposition on immunofluorescence).
Management
- Plasmapheresis
- Corticosteroids
- Cyclophosphamide.
Complications
- Rapidly progressive glomerulonephritis
- alveolar hemorrhage.