IgA Vasculitis (Henoch-Schonlein Purpura)

Rheumatology

Overview

Definition

Most common childhood vasculitis.

Epidemiology

Varies globally depending on genetics, environment, or exposure.

Etiology & Risk Factors

  • IgA immune complex deposition, often post-URI.

Clinical Symptoms

  • Palpable purpura on buttocks/legs
  • colicky abdominal pain
  • arthritis.

Clinical Approach

Diagnosis

  • Clinical
  • Skin/Renal biopsy (IgA deposition).

Management

  • Supportive care (NSAIDs)
  • Steroids for severe GI/renal disease.

Complications

  • Intussusception
  • IgA nephropathy.