Overview
Definition
Progressive inflammatory myopathy in older adults.
Epidemiology
Varies globally depending on genetics, environment, or exposure.
Etiology & Risk Factors
- Degenerative/Autoimmune.
Clinical Symptoms
- Asymmetric distal and proximal muscle weakness
- poor grip strength.
Clinical Approach
Diagnosis
- Muscle biopsy (rimmed vacuoles).
Management
- Generally resistant to immunosuppression
- Physical therapy.
Complications
- Severe disability
- dysphagia.