Overview
Definition
Inherited disorder causing tumors in endocrine glands.
Epidemiology
Varies globally. Often age and lifestyle dependent.
Etiology & Risk Factors
- Mutation in MEN1 gene (autosomal dominant).
Clinical Symptoms
- 3 P's: Parathyroid (hypercalcemia)
- Pituitary (prolactinoma)
- Pancreatic (gastrinoma).
Clinical Approach
Diagnosis
- Genetic testing
- hormone levels
- imaging.
Management
- Surgical resection of tumors
- medical management.
Complications
- Malignancy
- severe peptic ulcer disease (Zollinger-Ellison).