Primary Aldosteronism (Conn's Syndrome)

Endocrinology

Overview

Definition

An endocrine disorder characterized by the autonomous, excessive production of aldosterone from the adrenal cortex, leading to hypertension and hypokalemia.

Epidemiology

Underdiagnosed cause of hypertension; accounts for 5-10% of all hypertensive patients.

Etiology & Risk Factors

  • Adrenal adenoma (Conn's Syndrome, 30-40%)
  • Bilateral adrenal hyperplasia (60%)
  • Adrenal carcinoma (rare)

Clinical Symptoms

  • Treatment-resistant hypertension
  • Muscle weakness and cramps (due to hypokalemia)
  • Polydipsia and polyuria

Clinical Approach

Diagnosis

  • Screening: Elevated Aldosterone-to-Renin Ratio (ARR > 20-30)
  • Confirmation: Oral salt loading or saline infusion test showing failure to suppress aldosterone
  • CT Adrenals and adrenal venous sampling (AVS) to localize

Management

  • Unilateral adenoma: Surgical adrenalectomy
  • Bilateral hyperplasia: Aldosterone antagonists (Spironolactone, Eplerenone)

Complications

  • Left ventricular hypertrophy
  • Stroke / Cardiovascular disease
  • Chronic Kidney Disease
  • Atrial Fibrillation