Overview
Definition
Inflammation, stricturing, and fibrosis of intra/extrahepatic bile ducts.
Epidemiology
Varies globally depending on genetics, environment, or exposure.
Etiology & Risk Factors
- Autoimmune, strongly associated with Ulcerative Colitis (>80%).
Clinical Symptoms
- Pruritus
- jaundice
- fatigue.
Clinical Approach
Diagnosis
- MRCP/ERCP (beaded appearance of bile ducts).
Management
- Endoscopic dilation of strictures
- Liver transplant.
Complications
- Cholangiocarcinoma
- Liver cirrhosis.