Overview
Definition
Severe, life-threatening mucocutaneous hypersensitivity reaction.
Epidemiology
Varies globally depending on genetics, environment, or exposure.
Etiology & Risk Factors
- Medications (Allopurinol, Anticonvulsants, Sulfonamides).
Clinical Symptoms
- Fever
- painful coalescing targetoid lesions
- mucosal ulceration (lips/eyes)
- <10% body surface area detachment.
Clinical Approach
Diagnosis
- Clinical
- Skin biopsy.
Management
- Immediate cessation of offending drug
- Burn unit care
- IVIG.
Complications
- Blindness
- massive sepsis
- death.