Overview
Definition
Granulomatous vasculitis of the aorta and its major branches.
Epidemiology
Varies globally depending on genetics, environment, or exposure.
Etiology & Risk Factors
- Autoimmune (affects young Asian women).
Clinical Symptoms
- Weak/absent pulses in upper extremities
- claudication
- bruits.
Clinical Approach
Diagnosis
- MRA or CTA (aortic thickening/narrowing).
Management
- High-dose corticosteroids.
Complications
- Aortic aneurysm
- stroke
- myocardial infarction.