Wernicke-Korsakoff Syndrome

Neurology

Overview

Definition

Neurologic complication of severe Thiamine (Vitamin B1) deficiency.

Epidemiology

Varies globally depending on genetics, environment, or exposure.

Etiology & Risk Factors

  • Chronic alcoholism, severe malnutrition.

Clinical Symptoms

  • Wernicke: Confusion
  • Ophthalmoplegia
  • Ataxia. Korsakoff: Confabulation
  • permanent memory loss.

Clinical Approach

Diagnosis

  • Clinical
  • low RBC transketolase activity.

Management

  • IV Thiamine BEFORE glucose administration.

Complications

  • Permanent severe anterograde amnesia (Korsakoff).